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Pulmonary-involvement as initial manifestation of Pediatric-Sjögren

Sieiro Santos

Sjögren’s syndrome is a systemic autoimmune disease caused by lymphocytic infiltration of exocrine glands causing sicca syndrome. It can affect extra-glandular organs such as the lungs which can result in diffuse interstitial lung disease, a well-known form of lung involvement. In pediatric patients, Sjögren’s syndrome is less common that in adult patients and often associates more heterogeneous presentations.